The Journal of Bucharest College of Physicians and the Romanian Academy of Medical Sciences

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A Rare Tumor - Primary Leiomyosarcoma of Pulmonary Artery. Case Presentation

2016-02

Laura Rebegea, Dorel Firescu, Mihaela Dumitru, Alina Mihaela Calin, Rodica Anghel

Pulmonary artery sarcomas (PA) are uncommon; the first case was documented in 1923 by Mandel Staam. Leiomyosarcoma, fibrosarcoma and rhabdomyosarcoma are the most often histologically confirmed incidences. PA tumor is frequently misinterpreted as thrombo-embolism, as its correct diagnosis is difficult. Magnetic Resonance Imaging (MRI) is superior in providing an accurate diagnosis. Surgery is the only therapeutic strategy which may extend life expectancy. The survival rate in the absence of surgical care is of 1.5 months, survival for 5 years - 6%. In most cases, death occurs by heart failure, and rarely by distant metastases. [...]

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